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Rigid Spine Syndrome: A Clinical Symptom Encompassing Various Aethiologies

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  • Giovanni Antioco Putzu

    (Department of Neurology and Clinical Neurophysiology, Italy)

Abstract

The rigid spine syndrome (R.S.S.) is an unusual muscular disorder, which typical features include a reduction of the spine flexion and fibrous degeneration of axial muscles. This rare manifestation may be associated with miscellaneous conditions. We report two cases of R.S.S, one linked to desmine accumulation myopathy and another due to pseudohypoparathyroidism. Spinal muscle involvement was associated with muscular weakness of the limbs in the former; in contrast muscle strength was normal in the latter. Both had increased levels of creatine kinase (CK), respectively of 624 I.U/l and 1648 I.U/l. To our knowledge the case of rigid spine syndrome associated with pseudohypoparathyroidism is unique, whereas the link of this syndrome with miscellaneous muscle disorders is much more usual. In addition, the pivotal role of calcium on CK increase is further clarify and confirmed by normalization of CK value after calcium therapy in the patient affected by pseudohypoparathyroidism. Although none had spinal deformities and thus, no indication for surgical correction, both are of clinical interest for the orthopaedics which may manage with patients presenting R.S.S.

Suggested Citation

  • Giovanni Antioco Putzu, 2017. "Rigid Spine Syndrome: A Clinical Symptom Encompassing Various Aethiologies," Current Trends in Clinical & Medical Imaging, Juniper Publishers Inc., vol. 1(1), pages 15-17, February.
    • Handle: RePEc:adp:jctcmi:v:1:y:2017:i:1:p:15-17
    DOI: 10.19080/CTCMI.2017.01.555555
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