IDEAS home Printed from
   My bibliography  Save this paper

Understanding the costs of care for cystic fibrosis: an analysis by age and severity. CHERE Working Paper 2011/1


  • Kees Van Gool
  • Richard Norman

    () (CHERE, University of Technology, Sydney)

  • Martin B Delatycki
  • Jane Hall

    () (CHERE, University of Technology, Sydney)

  • John Massie


Cystic fibrosis (CF) is the most common life-shortening genetic disease, with an incidence of 1 in 2500 and carrier frequency of 1 in 25, amongst Caucasians (Welsh, Ramsey et al. 2001). With recent advances in treatment, most children with CF now can expect to survive into adulthood and life expectancy has improved considerably. CF is a progressive disease which affects many organ systems and as the disease progresses patients require more intensive health care that includes home based care and medications, along with more frequent and prolonged hospital admissions, and in around half of all cases lung transplantation.(Jason, Leah et al. 2009; Paul, Leah et al. 2009). As new and improving treatment options become available, the pattern of care will change, which will impact on the costs of treatment and on patient outcomes. For example, two of the key medications developed in the last 15 years, Pulmozyme and TOBI (not licensed for use in Australia) cost A$14,000 pa; and more sophisticated technology, such as gene-based treatments will be equally, or more expensive. Thus health care policy makers and funders will expect rigorous assessments of the cost-effectiveness of new treatments.

Suggested Citation

  • Kees Van Gool & Richard Norman & Martin B Delatycki & Jane Hall & John Massie, 2011. "Understanding the costs of care for cystic fibrosis: an analysis by age and severity. CHERE Working Paper 2011/1," Working Papers 2011/1, CHERE, University of Technology, Sydney.
  • Handle: RePEc:her:chewps:2011/1

    Download full text from publisher

    File URL:
    File Function: First version,
    Download Restriction: no


    Citations are extracted by the CitEc Project, subscribe to its RSS feed for this item.

    Cited by:

    1. Ilene L. Hollin & Karen A. Robinson, 2016. "A Scoping Review of Healthcare Costs for Patients with Cystic Fibrosis," Applied Health Economics and Health Policy, Springer, vol. 14(2), pages 151-159, April.
    2. Yuanyuan Gu & Sonia García-Pérez & John Massie & Kees Gool, 2015. "Cost of care for cystic fibrosis: an investigation of cost determinants using national registry data," The European Journal of Health Economics, Springer;Deutsche Gesellschaft für Gesundheitsökonomie (DGGÖ), vol. 16(7), pages 709-717, September.

    More about this item


    Cystic Fibrosis; costs; cost effectiveness;

    JEL classification:

    • I19 - Health, Education, and Welfare - - Health - - - Other

    NEP fields

    This paper has been announced in the following NEP Reports:


    Access and download statistics


    All material on this site has been provided by the respective publishers and authors. You can help correct errors and omissions. When requesting a correction, please mention this item's handle: RePEc:her:chewps:2011/1. See general information about how to correct material in RePEc.

    For technical questions regarding this item, or to correct its authors, title, abstract, bibliographic or download information, contact: (Liz Chinchen). General contact details of provider: .

    If you have authored this item and are not yet registered with RePEc, we encourage you to do it here. This allows to link your profile to this item. It also allows you to accept potential citations to this item that we are uncertain about.

    We have no references for this item. You can help adding them by using this form .

    If you know of missing items citing this one, you can help us creating those links by adding the relevant references in the same way as above, for each refering item. If you are a registered author of this item, you may also want to check the "citations" tab in your RePEc Author Service profile, as there may be some citations waiting for confirmation.

    Please note that corrections may take a couple of weeks to filter through the various RePEc services.

    IDEAS is a RePEc service hosted by the Research Division of the Federal Reserve Bank of St. Louis . RePEc uses bibliographic data supplied by the respective publishers.