Congenital Intrahepatic Portal Vein Aneurysm Associated with Left Kidney Hypoplasia as Incidental Imaging Findings in An Adult– A Case Study

Background: Intrahepatic portal vein aneurysm is a rare condition, considered in less than 3% of all venous aneurysms, and may have a congenital or acquired etiology; another congenital pathology, such as renal hypoplasia occurs in approximately 2.2% of the population, with prenatal or postnatal diagnosis. Case Presentation: We present a rare case to our knowledge, without a correspondent in the literature, which developed both malformations, incidentally diagnosed using Doppler ultrasound and multidetector computed tomography, in an adult female patient with nonspecific abdominal discomfort. The absence of any complications and the stable evolution during three years of follow-up were the arguments for congenital pathology. Conclusion: This case illustrates a couple of rarely associated malformations represented by portal vein aneurysm and renal hypoplasia, the usefulness and limitations of Doppler ultrasound as the first method recommended in the diagnosis and follow-up, and the superior results of multidetector computed tomography as a complementary tool.