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Living with Phenylketonuria: Perspectives of Patients and Their Families

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Author Info
Cihan Bilginsoy
Norman Waitzman
Claire O. Leonard
Sharon L. Ernst

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Abstract

This study surveyed PKU patients and their primary caretakers to assess their current management practices, the barriers to effective management, and the potential utility of a home monitor in managing PKU. A survey instrument was mailed to caretakers of all 50 patients with PKU in Utah between the ages of 2 and 18 in 1997 (response rate: 64%). It included separate components for caretakers and patients aged 10 to 18. While there was uneven compliance with recommended practices, caretakers universally recognized the negative consequences of not adhering to the low-protein diet. There was, however, disagreement regarding such consequences among the older children surveyed. The primary obstacles cited to better adherence were time constraints and stress associated with food preparation and record-keeping, and the restrictions imposed on social life. Phe test results were regarded as the principal signal for the need for dietary adjustment. A home monitor, it was widely agreed, would facilitate better management through more regular and timely feedback. Despite the facts that obstacles to dietary adherence are multifaceted and that no single intervention would therefore serve as a panacea, a large majority of respondents believed that a home monitor to be an important contributor to the successful management of PKU.

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Publisher Info
Paper provided by University of Utah, Department of Economics in its series Working Paper Series, Department of Economics, University of Utah with number 2004_04.

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Length: 22 pages
Date of creation: Apr 2004
Date of revision:
Publication status: Published in Journal of Inherited Metabolic Disease, January, Vol 28, pp.639-649
Handle: RePEc:uta:papers:2004_04

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Postal: 1645 E. Central Campus Dr. Front, Salt Lake City, UT 84112-9300
Phone: (801) 581-7481
Fax: (801) 585-5649
Web page: http://www.econ.utah.edu
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Related research
Keywords: Phenylketonuria; dietary management; self-monitoring;

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Find related papers by JEL classification:
I18 - Health, Education, and Welfare - - Health - - - Government Policy; Regulation; Public Health
I19 - Health, Education, and Welfare - - Health - - - Other

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References listed on IDEAS
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  1. Norman Waitzman & Cihan Bilginsoy & Claire O. Leonard & Sharon L. Ernst & Annie Prince, 2004. "The Effect of Phenylalanine Test Frequency on Management of Phenylketonuria (PKU)," Working Paper Series, Department of Economics, University of Utah 2004_03, University of Utah, Department of Economics. [Downloadable!]
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  1. Norman Waitzman & Cihan Bilginsoy & Claire O. Leonard & Sharon L. Ernst & Annie Prince, 2004. "The Effect of Phenylalanine Test Frequency on Management of Phenylketonuria (PKU)," Working Paper Series, Department of Economics, University of Utah 2004_03, University of Utah, Department of Economics. [Downloadable!]
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This page was last updated on 2009-12-13.


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